ULTRASOUND DIAGNOSIS OF NONCOMPACTION OF THE LEFT VENTRICULAR MYOCARDIUM
Rubrics: CASE REPORT
Authors:
1.
Irkutsk State Regional Children’s Clinical Hospital
( Ultrasonic Medical Investigation Specialist)
Irkutsk, Irkutsk region, Russian Federation
Irkutsk, Irkutsk region, Russian Federation
2.
Irkutsk State Medical Academy of Postgraduate Education
( Head of the Department of Pediatrics)
Irkutsk, Irkutsk region, Russian Federation
Irkutsk, Irkutsk region, Russian Federation
3.
Irkutsk State Medical Academy of Postgraduate Education
( Teaching Assistant at the Department of Pediatrics)
Irkutsk, Irkutsk region, Russian Federation
Irkutsk, Irkutsk region, Russian Federation
4.
Irkutsk, Irkutsk region, Russian Federation
Type:
Article
Pages:
from 186
to 192
Status:
Published
Received:
18.10.2017
Accepted:
10.01.2023
Published:
22.11.2017
Subject area:
UDK 61 Медицина. Охрана здоровья
Language:
Russian
Keywords:
ul'trazvukovaya diagnostika, kardiomiopatiya, nekompaktnyy miokard levogo zheludochka, ehokardiografiya, deti
Abstract (English):
Opisany klinicheskie sluchai redko vstrechayuschegosya, geneticheski geterogennoy kardiomiopatii – nekompaktnogo miokarda levogo zheludochka u 4 detey (3 mal'chika i 1 devochka) v vozraste ot 2 mesyacev do 6 let. Predstavleno opisanie ehokardiograficheskoy kartiny v sootvetstvii s sovremennymi diagnosticheskimi kriteriyami. Nekompaktnyy miokard levogo zheludochka vyyavlen u 3, levogo i pravogo zheludochka – u 1. Sredi 4 pacientov u 3 nekompaktnyy miokard byl samostoyatel'nym zabolevaniem, a esche u 1 on vyyavlen na fone neyrofibromatoza I tipa, v sochetanii s dilataciey koronarnyh arteriy i perikardial'nym vypotom. Troe iz 4 pacientov postupili s yavleniyami tyazheloy serdechnoy nedostatochnosti 3-4 FK po NYHA. Privedeny ehokardiogrammy s opisaniem harakternyh osobennostey zabolevaniya (gipertrabekulyarnost', gubchatyy miokarda, tipichnoe sootnoshenie nekompaktnogo i kompaktnogo sloya ot 2,0 do 2,6. Vsem 4 pacientam byli naznacheny preparaty dlya lecheniya serdechnoy nedostatochnosti (diuretiki, beta-blokatory, kapoten, v odnom sluchae digoksin); dvoe poluchali antitromboticheskuyu terapiyu (aspirin, varfarin). Privedeny rezul'taty dinamicheskogo nablyudeniya pacientov s NMLZh v techenie neskol'kih let na fone lecheniya s ocenkoy razlichiy ul'trazvukovoy kartiny. U 2 pacientov iz 4 detey na fone terapii zastoynoy serdechnoy nedostatochnosti pri nablyudenii ≥ 5 let frakciya izgnaniya levogo zheludochka vozrosla – kak po Simpson, tak i po Teicholz, odnovremenno so snizheniem stepeni serdechnoy nedostatochnosti; a esche u 2 pri nablyudenii ot 2 mes. do 5 let frakciya izgnaniya levogo zheludochka tozhe uvelichilas', no sohranyaetsya zastoynaya serdechnaya nedostatochnost' 3 FK i priznaki pravozheludochkovoy nedostatochnosti.
Opisany klinicheskie sluchai redko vstrechayuschegosya, geneticheski geterogennoy kardiomiopatii – nekompaktnogo miokarda levogo zheludochka u 4 detey (3 mal'chika i 1 devochka) v vozraste ot 2 mesyacev do 6 let. Predstavleno opisanie ehokardiograficheskoy kartiny v sootvetstvii s sovremennymi diagnosticheskimi kriteriyami. Nekompaktnyy miokard levogo zheludochka vyyavlen u 3, levogo i pravogo zheludochka – u 1. Sredi 4 pacientov u 3 nekompaktnyy miokard byl samostoyatel'nym zabolevaniem, a esche u 1 on vyyavlen na fone neyrofibromatoza I tipa, v sochetanii s dilataciey koronarnyh arteriy i perikardial'nym vypotom. Troe iz 4 pacientov postupili s yavleniyami tyazheloy serdechnoy nedostatochnosti 3-4 FK po NYHA. Privedeny ehokardiogrammy s opisaniem harakternyh osobennostey zabolevaniya (gipertrabekulyarnost', gubchatyy miokarda, tipichnoe sootnoshenie nekompaktnogo i kompaktnogo sloya ot 2,0 do 2,6. Vsem 4 pacientam byli naznacheny preparaty dlya lecheniya serdechnoy nedostatochnosti (diuretiki, beta-blokatory, kapoten, v odnom sluchae digoksin); dvoe poluchali antitromboticheskuyu terapiyu (aspirin, varfarin). Privedeny rezul'taty dinamicheskogo nablyudeniya pacientov s NMLZh v techenie neskol'kih let na fone lecheniya s ocenkoy razlichiy ul'trazvukovoy kartiny. U 2 pacientov iz 4 detey na fone terapii zastoynoy serdechnoy nedostatochnosti pri nablyudenii ≥ 5 let frakciya izgnaniya levogo zheludochka vozrosla – kak po Simpson, tak i po Teicholz, odnovremenno so snizheniem stepeni serdechnoy nedostatochnosti; a esche u 2 pri nablyudenii ot 2 mes. do 5 let frakciya izgnaniya levogo zheludochka tozhe uvelichilas', no sohranyaetsya zastoynaya serdechnaya nedostatochnost' 3 FK i priznaki pravozheludochkovoy nedostatochnosti.
Keywords:
ul'trazvukovaya diagnostika, kardiomiopatiya, nekompaktnyy miokard levogo zheludochka, ehokardiografiya, deti
ul'trazvukovaya diagnostika, kardiomiopatiya, nekompaktnyy miokard levogo zheludochka, ehokardiografiya, deti
1. Spislit ehokardiografiya
